News tagged with inherited prion
Mouse model of prion disease mimics diverse symptoms of human disorder
Nov 26, 2008 |
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A comprehensive mouse model of inherited prion disease exhibits cognitive, motor, and neurophysiological deficits that bear a striking resemblance to the symptoms experienced by patients with the human version of "mad cow ...
Search results for inherited prion
Iron is involved in prion disease-associated neuronal demise
Mar 13, 2009 |
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Imbalance of iron homeostasis is a common feature of prion disease-affected human, mouse, and hamster brains, according to a new study by Dr. Neena Singh and colleagues at Case Western Reserve University School of Medicine, ...
Prion protein identified as a novel early pancreatic cancer biomarker
Aug 17, 2009 |
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Mad cow disease is caused by the accumulation of an abnormal protein, the prion, in the brain of an affected patient. Outside of the brain, very little is known about prions. Case Western Reserve University School of Medicine, ...
Study points to disruption of copper regulation as key to prion diseases
Apr 17, 2009 |
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(PhysOrg.com) -- An investigation of a rare, inherited form of Creutzfeldt-Jakob disease suggests that disrupted regulation of copper ions in the brain may be a key factor in this and other prion diseases.
Scientists uncover evolutionary origins of prion disease gene
Sep 28, 2009 |
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A University of Toronto-led team has uncovered the evolutionary ancestry of the prion gene, which may reveal new understandings of how the prion protein causes diseases such as bovine spongiform encephalopathy (BSE), also ...
Prions serve as important source of variation in nature
Apr 02, 2009 |
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Special proteins known as prions, which are perhaps best known as the agents of mad cow and other neurodegenerative diseases, can also serve as an important source of beneficial variation in nature, confirms a new study in ...
A penny for your prions: Researchers study link between copper, mad cow disease
Jun 25, 2009 |
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(PhysOrg.com) -- North Carolina State University researchers have discovered a link between copper and the normal functioning of prion proteins, which are associated with transmissible spongiform encephalopathy ...
Impaired transport in neurons triggers prion disease
Aug 21, 2009 |
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A new study shows that nervous system integrity and axonal properties may play a key role in prion diseases. The findings, from researchers at the Rudolf Virchow Center and the Institute of Virology of the University of Würzburg, ...
The protein Srebp2 drives cholesterol formation in prion-infected neuronal cells
Nov 18, 2009 |
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Prions are causing fatal and infectious diseases of the nervous system, such as the mad cow disease (BSE), scrapie in sheep or Creutzfeldt-Jakob disease in humans. Scientists of Helmholtz Zentrum München and Technische Universität ...
Gene mutation alone causes transmissible prion disease
Medicine & Health / Neuroscience
Aug 26, 2009 |
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For the first time, Whitehead Institute researchers have shown definitively that mutations associated with prion diseases are sufficient to cause a transmissible neurodegenerative disease.
Researchers find new piece of BSE puzzle
Nov 20, 2009 |
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A new treatment route for bovine spongiform encephalopathy (BSE) and its human form Creutzfeldt Jakob disease (CJD) could be a step closer based on new results from scientists at the University of Leeds. The team has found ...
List of search results for inherited prion
